Journal Article IgA Nephropathy Complicated with X-linked Thrombocytopenia

Kakio, Yuki  ,  A. Uchida, Haruhito  ,  Kitagawa, Masashi  ,  Arata, Yuka  ,  Kato, Ayako  ,  Inoue-Torii, Akiko  ,  Hinamoto, Norikazu  ,  Ogawa-Akiyama, Ayu  ,  Sugiyama, Hitoshi  ,  Wada, Jun

72 ( 3 )  , pp.301 - 307 , 2018-06 , Okayama University Medical School
Renal involvement is occasionally observed in Wiskott-Aldrich syndrome (WAS) and X-linked thrombocytopenia (XLT). It has been reported that galactose-deficient IgA is a closely linked to IgA nephropathy (IgAN), suggesting that patients with XLT/WAS associated with reduced galactosylation on serum IgA are susceptible to IgAN. It is necessary to pay more attention to patients with IgAN due to the potential complication with XLT/WAS. We here present a patient of XLT complicated with mild IgAN who underwent tonsillectomy combined with steroid pulse therapy to achieve complete clinical remission.

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